AMINO ACID SUBSTITUTION
In addition to phenylalanine, our body requires 19 other amino acids. Most foodstuffs of plant and animal origin contain these amino acids.
However, persons with PKU cannot break down the amino acid phenylalanine, so that when they eat a normal diet, excessive levels of phenylalanine accumulate in their bodies. To prevent this, the treatment for PKU requires strict compliance with a diet low in phenylalanine, i.e. persons with PKU must follow a strict low-protein diet. However, this means that they are missing out on all the other essential building blocks of protein.
Thus, persons with PKU must take a dietary supplement that consists of a mixture containing all of the important amino acids except for phenylalanine.
It also contains vitamins, minerals and trace elements to ensure normal physical and mental development.